Absence of pulmonic valve associated with double-outlet right ventricle.

ABSENCE of the pulmonic valve is a rare congenital lesion which is usually associated with tetralogy of Fallot." 2 We have recently observed a patient in whom this anomaly coexisted with "double-outlet right ventricle." This case is reported because a review of the literature has failed to reveal a similar case and because certain difficulties inherent in the differentiation of double-outlet right ventricle with right ventricular obstruction from tetralogy of Fallot are well illustrated by this case.